A common cause of intensely itchy erythroderma in infants and children, often with significant weeping and crusting.
A rare infection acquired in utero, presenting at birth with a generalized eruption of erythematous macules, papules, and pustules that can be confluent.
Several forms, such as lamellar ichthyosis or congenital ichthyosiform erythroderma, present at birth with generalized erythema and scale, often as a "collodion baby".
A type of ichthyosis characterized from birth by generalized redness and fine white scale, with less severe hyperkeratosis than lamellar ichthyosis.
A form of chondrodysplasia punctata with a characteristic swirled or linear pattern of ichthyosiform erythroderma along Blaschko's lines.
Presents in infancy as a thickened, doughy, yellowish erythroderma that exhibits a dramatic Darier's sign (urtication and blistering on rubbing).
A genetic ichthyosis presenting at birth with erythroderma and blistering, which later evolves into severe, verrucous hyperkeratosis.
A genetic disorder characterized by congenital ichthyosis, a specific hair shaft defect (trichorrhexis invaginata), and severe atopic dermatitis-like erythroderma.
A severe combined immunodeficiency (SCID) presenting in early infancy with erythroderma, alopecia, lymphadenopathy, and failure to thrive.
Juvenile PRP can cause an erythroderma with a characteristic orange-red hue, islands of sparing, and follicular keratosis.
Can cause erythroderma in children, appearing as generalized bright red skin, though it is less common than in adults.
Severe infantile seborrheic dermatitis can become generalized, leading to an erythroderma with greasy scale, particularly on the scalp and in flexures.
A toxin-mediated disease causing diffuse, tender erythema followed by widespread superficial blistering and exfoliation of the epidermis in sheets.
An X-linked immunodeficiency with a classic triad of thrombocytopenia, immunodeficiency, and a severe, intractable eczematous rash that can become erythrodermic.
