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Antiphospholipid syndrome

An autoimmune disorder that can cause a net-like or starburst pattern of purpura and necrosis due to thrombosis.

Brown recluse spider bite

The bite classically causes a lesion with a central violaceous area surrounded by a pale ring of ischemia and an outer red ring, which can have a retiform pattern.

Calciphylaxis

A condition of vascular calcification and thrombosis, leading to intensely painful, violaceous, retiform purpura that progresses to necrotic ulcers with black eschars.

Cholesterol emboli

Showering of cholesterol crystals from an atherosclerotic plaque can cause a livedo reticularis pattern and painful, purpuric 'blue toe syndrome'.

Cryoglobulinaemia

A vasculitis that can occlude larger vessels, leading to retiform purpura and necrosis, in addition to typical palpable purpura.

Ecthyma gangrenosum

A cutaneous sign of Pseudomonas sepsis, which can present as multiple hemorrhagic pustules that evolve into necrotic ulcers with a retiform border.

Heparin necrosis

A rare reaction to heparin causing well-demarcated, painful, hemorrhagic plaques with a retiform border that progress to necrosis.

Intravascular B cell lymphoma

A rare lymphoma where malignant cells proliferate within blood vessels, causing occlusion and presenting as tender, indurated, purpuric plaques with a retiform pattern.

Pancreatic panniculitis

Can cause tender nodules that ulcerate, sometimes with a surrounding retiform purpuric pattern.

Polyarteritis nodosa

A medium-vessel vasculitis that characteristically causes tender subcutaneous nodules and a 'starburst' or broken-net pattern of livedo (livedo racemosa).

Sickle cell crisis

Vaso-occlusion from sickled red blood cells can cause painful leg ulcers with a surrounding retiform purpuric pattern.

Vasculitis

While typically causing palpable purpura, vessel occlusion in certain vasculitides (like ANCA-associated vasculitis) can lead to larger, net-like patterns of purpura and necrosis.

Veno-occlusive

A general term for purpura caused by occlusion of veins, leading to a net-like pattern, as seen in various hypercoagulable states.

Warfarin necrosis

A rare complication of warfarin therapy, presenting as painful, hemorrhagic skin lesions with a retiform border that progress to necrosis.

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