An inherited periodic fever syndrome where attacks of urticarial rash and fever are specifically triggered by exposure to cold.
An inherited autoinflammatory disorder characterized by recurrent episodes of fever and painful polyserositis (abdominal, chest, or joint pain).
An inherited periodic fever syndrome causing recurrent urticaria, fever, and arthralgia, often leading to progressive sensorineural hearing loss and amyloidosis.
The most severe cryopyrin-associated periodic syndrome, present from infancy with chronic urticaria, fever, and severe arthropathy and CNS inflammation.
Follows a Group A Streptococcus infection and is diagnosed by the Jones criteria, including carditis, polyarthritis, and erythema marginatum, not an evanescent rash.
An inherited autoinflammatory syndrome characterized by prolonged febrile episodes (weeks), migratory myalgia, and a characteristic periorbital edema.
Common urticaria consists of transient, pruritic wheals that last for hours, unlike the evanescent, salmon-pink, non-pruritic rash of Still's disease that coincides with fever spikes.
Presents with urticarial lesions that are painful or burning, last longer than 24 hours, and may leave behind bruising (purpura) on resolution.
